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KMID : 1103720190800030537
Journal of the Korean Society of Radiology
2019 Volume.80 No. 3 p.537 ~ p.542
A Rare Case of Granulomatosis with Polyangiitis-Related Periaortitis at the Ascending Aorta
Hong Sang-Hyup

Hong Gil-Sun
Lee Choong-Wook
Kim Gi-Hong
Abstract
Acute aortic syndrome including intramural hematoma is a life-threatening disease encountered in the emergency department with high in-hospital mortality even when a timely diagnosis is made. Therefore, accurate differential diagnosis of acute aortic syndrome and its mimics is important to determine the patient's treatment plan. Until now, a few pathologic diseases mimicking aortic intramural hematoma such as periaortic lymphoma and immunoglobulin G4-elated periaoritis have been reported. Here, we report a rare case of granulomatosis with polyangiitis-related periaortitis misdiagnosed as aortic intramural hematoma presenting to the emergency department with chest pain and similar radiologic findings.
KEYWORD
Granulomatosis With Polyangiitis, Aortic Diseases, Vasculitis, Spiral CT, PET-CT
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